Abstract
Primary Pachydermoperiostosis is a rare hereditary disease characterized by folded coarse
skin, hyperostosis, clubbing and abnormality in other organ such as gastrointestinal tract.
This syndrome is autosomal dominant with variable expressivity, but a family with autosomal
recessive had also been reported. Disease occurs predominantly in men. Secondary form is
usually a provoked by sever pulmonary disease. Treatment is symptomatic. This is a case report
of such patient from Baloochestan, Iran.
skin, hyperostosis, clubbing and abnormality in other organ such as gastrointestinal tract.
This syndrome is autosomal dominant with variable expressivity, but a family with autosomal
recessive had also been reported. Disease occurs predominantly in men. Secondary form is
usually a provoked by sever pulmonary disease. Treatment is symptomatic. This is a case report
of such patient from Baloochestan, Iran.
Keywords
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Copyright
© 2002, Author(s). This is an open-access article distributed under the terms of the Creative Commons Attribution 4.0 International License (CC BY 4.0) (https://creativecommons.org/licenses/by/4.0/) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.