Abstract
Primary Pachydermoperiostosis is a rare hereditary disease characterized by folded coarse
skin, hyperostosis, clubbing and abnormality in other organ such as gastrointestinal tract.
This syndrome is autosomal dominant with variable expressivity, but a family with autosomal
recessive had also been reported. Disease occurs predominantly in men. Secondary form is
usually a provoked by sever pulmonary disease. Treatment is symptomatic. This is a case report
of such patient from Baloochestan, Iran.
skin, hyperostosis, clubbing and abnormality in other organ such as gastrointestinal tract.
This syndrome is autosomal dominant with variable expressivity, but a family with autosomal
recessive had also been reported. Disease occurs predominantly in men. Secondary form is
usually a provoked by sever pulmonary disease. Treatment is symptomatic. This is a case report
of such patient from Baloochestan, Iran.
Keywords
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Copyright
© 2002, Author(s). This open-access article is available under the Creative Commons Attribution 4.0 (CC BY 4.0) International License (https://creativecommons.org/licenses/by/4.0/), which allows for unrestricted use, distribution, and reproduction in any medium, provided that the original work is properly cited.