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36 resultsUpdated October 20, 2026
1

Guía de Práctica Clínica para el manejo nutricional de personas con Fibrosis Quística (GPC-FQ)

Revista Española de Nutrición Humana y Dietética 21(1) (2017)

María Garriga; Adriana Horrisberger; Arantza Ruiz de las Heras de la Hera; Natalia Catalán; Gloria Fernández; Marta Suárez; Nuria Porras; Laura Monje

2

Evolving Cystic Fibrosis Care: Lung Immunology and Emerging Health Challenges in the Era of CFTR Modulators

Biomolecules 15(10) (2025)

Giuseppe Fabio Parisi; Maria Papale; Giulia Pecora; Santiago Presti; Monica Tosto; Enza Mulé; Vittorio Ornato; Donatella Aloisio; Salvatore Leonardi

3

Liver Disease in Cystic Fibrosis

Practical Hepatic Pathology: a Diagnostic Approach (2018)

Pierre Russo

4

Neonatal cholestasis: recent insights

Egyptian Pediatric Association Gazette 67(1) (2019)

Ramy Mohamed Ghazy; Mohamed Ahmed Khedr

5

Longitudinal Transient Elastography Measurements Used in Follow-up for Patients with Cystic Fibrosis

Ultrasound in Medicine & Biology 42(4) (2016)

Stephanie Van Biervliet; Hugo Verdievel; Saskia Vande Velde; Ruth De Bruyne; Danny De Looze; Xavier Verhelst; Anja Geerts; Eddy Robberecht; Hans Van Vlierberghe

6

Pediatric Liver Disease

Practical Gastroenterology and Hepatology Board Review Toolkit (2016)

Tamir Miloh

7

Ursodeoxycholic acid for cystic fibrosis-related liver disease

Cochrane Database of Systematic Reviews (1999)

Katharine Cheng; Deborah Ashby; Rosalind L Smyth

8

Drug-Induced Vanishing Bile Duct Syndrome: From Pathogenesis to Diagnosis and Therapeutics

Seminars in Liver Disease 41(03) (2021)

Fernando Bessone; Nelia Hernández; Mario Tanno; Marcelo G. Roma

9

Focus on gastroesophageal reflux disease in patients with cystic fibrosis

World Journal of Gastroenterology 26(41) (2020)

Annarita Bongiovanni; Sara Manti; Giuseppe Fabio Parisi; Maria Papale; Enza Mulè; Novella Rotolo; Salvatore Leonardi

10

Isolated liver disease in a patient with a CFTR genotype F508del/12TG-5T and 470MV: A new face of an old disease

Annals of Hepatology 14(6) (2015)

Andrea D. Praticò; Elena R. Praticò; Novella Rotolo; Stefania Salafia; Chiara Franzonello; Salvatore Leonardi

11

Analysis of a large cohort of cystic fibrosis patients with severe liver disease indicates lung function decline does not significantly differ from that of the general cystic fibrosis population

PLOS ONE 13(10) (2018)

Deepika Polineni; Annalisa V. Piccorelli; William B. Hannah; Sarah N. Dalrymple; Rhonda G. Pace; Peter R. Durie; Simon C. Ling; Michael R. Knowles; Jaclyn R. Stonebraker

12

Microgallbladder: Self-Remitting Acute Cholecystitis-Like Condition Unique to Patients with Cystic Fibrosis

Case Reports in Radiology 2019 (2019)

Mina S. Mousa; John C. Feldman; Paresh Mahajan

13

A novel free-breathing abdominal RAVE T2/T1 hybrid MRI sequence in patients with cystic fibrosis: Preliminary results

European Journal of Radiology 154 (2022)

Katja Glutig; Paul-Christian Krüger; Theresa Oberreuther; Ulf Teichgräber; Michael Lorenz; Hans-Joachim Mentzel; Martin Krämer

14

Current Practices and Potential Nanotechnology Perspectives for Pain Related to Cystic Fibrosis

Journal of Clinical Medicine 8(7) (2019)

Laura M. Trandafir; Magdalena M. Leon; Otilia Frasinariu; Ginel Baciu; Gianina Dodi; Elena Cojocaru

15

The Efficacy of MRI in the diagnostic workup of cystic fibrosis-associated liver disease: A clinical observational cohort study

European Radiology 29(2) (2018)

Sarah Poetter-Lang; Katharina Staufer; Pascal Baltzer; Dietmar Tamandl; Dina Muin; Nina Bastati; Emina Halilbasic; Jacqueline C. Hodge; Michael Trauner; Lili Kazemi-Shirazi; Ahmed Ba-Ssalamah

16

Pathologic Features of Hereditary Cholestatic Diseases

Surgical Pathology Clinics 11(2) (2018)

Andrew D. Clouston

17

Evaluation of noninvasive markers for the diagnosis of cystic fibrosis liver disease

Scandinavian Journal of Gastroenterology 53(12) (2018)

Alexandra Alexopoulou; Sophia Pouriki; Larisa Vasilieva; Theodoros Alexopoulos; Vasiliki Filaditaki; Maria Gioka; Filia Diamantea; Spyros P. Dourakis

18

Smoking resumption after heart or lung transplantation: a systematic review and suggestions for screening and management

Journal of Thoracic Disease 10(7) (2018)

Patrick Hofmann; Christian Benden; Malcolm Kohler; Macé M. Schuurmans

19

Dried Blood Spot-Based Metabolomic Profiling in Adults with Cystic Fibrosis

Journal of Proteome Research 19(6) (2020)

Wafa Al-Qahtani; Mai Abdel Jabar; Afshan Masood; Minnie Jacob; Imran Nizami; Majed Dasouki; Anas M. Abdel Rahman

20

Ursodeoxycholic acid for cystic fibrosis-related liver disease

Cochrane Database of Systematic Reviews (2014)

Katharine Cheng; Deborah Ashby; Rosalind L Smyth

21

Liver and Gallbladder

Clinical Anatomy of Digestive System a Handbook for Healthcare Professionals (2024)

Muhammed Furkan Arpaci

22

Lung Transplantation for Cystic Fibrosis: Results, Indications, Complications, and Controversies

Seminars in Respiratory and Critical Care Medicine 36(02) (2015)

David Sayah; John Belperio; S. Weigt; Joseph Lynch

23

Survival Benefits Following Liver Transplantation

Journal of Pediatric Gastroenterology and Nutrition 73(3) (2021)

Gunter Flemming; Ulrich Baumann; Nicolas Richter; Florian Vondran; Burkhard Tümmler; Anna‐Maria Dittrich; Carsten Müller; Mandy Vogel; Eva‐Doreen Pfister

24

Improvement of Hepatic Steatosis in Cystic Fibrosis With Ivacaftor Therapy

Journal of Pediatric Gastroenterology and Nutrition 60(5) (2015)

Don Hayes; Patrick S. Warren; Karen S. McCoy; Shahid I. Sheikh

25

The Potential Causes of Cystic Fibrosis-Related Diabetes

Frontiers in Endocrinology 12 (2021)

Lise Coderre; Lyna Debieche; Joëlle Plourde; Rémi Rabasa-Lhoret; Sylvie Lesage

26

Cystic fibrosis and portal hypertension: Distal splenorenal shunt can prevent the need for future liver transplant

Journal of Pediatric Surgery 54(5) (2019)

Caroline Lemoine; Joan Lokar; Susanna A. McColley; Estella M. Alonso; Riccardo Superina

27

Ursodeoxycholic acid for cystic fibrosis-related liver disease

Cochrane Database of Systematic Reviews 2021(4) (2017)

Katharine Cheng; Deborah Ashby; Rosalind L Smyth

28

Intestinal Inflammation and Alterations in the Gut Microbiota in Cystic Fibrosis: A Review of the Current Evidence, Pathophysiology and Future Directions

Journal of Clinical Medicine 11(3) (2022)

Rachel Y. Tam; Josie M. van Dorst; Isabelle McKay; Michael Coffey; Chee Y. Ooi

29

Fat-Soluble Vitamin Deficiency in Cystic Fibrosis

Diet and Exercise in Cystic Fibrosis (2015)

Vijay Karam Singh; Ronald Ross Watson

30

Cystic Fibrosis and Oxidative Stress: The Role of CFTR

Molecules 27(16) (2022)

Evelina Moliteo; Monica Sciacca; Antonino Palmeri; Maria Papale; Sara Manti; Giuseppe Fabio Parisi; Salvatore Leonardi

31

Cystic Fibrosis and Cancer: Unraveling the Complex Role of CFTR Gene in Cancer Susceptibility

Cancers 15(17) (2023)

Giuseppe Fabio Parisi; Maria Papale; Giulia Pecora; Novella Rotolo; Sara Manti; Giovanna Russo; Salvatore Leonardi

32

Aspartate aminotransferase to platelet ratio and fibrosis‐4 as biomarkers in biopsy‐validated pediatric cystic fibrosis liver disease

Hepatology 62(5) (2015)

Daniel H. Leung; Mahjabeen Khan; Charles G. Minard; Danielle Guffey; Louise E. Ramm; Andrew D. Clouston; Gregory Miller; Peter J. Lewindon; Ross W. Shepherd; Grant A. Ramm

33

Ursodeoxycholic acid for cystic fibrosis-related liver disease

Cochrane Database of Systematic Reviews (2012)

Katharine Cheng; Deborah Ashby; Rosalind L Smyth

35

Shear Wave Elastography in the Assessment of Liver Changes in Children with Cystic Fibrosis

Elastography - Applications in Clinical Medicine (2022)

Mikhail Pykov; Natalia Kuzmina; Nikolay Rostovtsev