Anesthetic management of patients with Klippel-Feil syndrome, a case series

Author(s):
Kamran MottaghiKamran MottaghiKamran Mottaghi ORCID1,*, Farhad SafariFarhad SafariFarhad Safari ORCID1, Parisa SezariParisa SezariParisa Sezari ORCID1, Naeime GholizadehNaeime Gholizadeh1, Masoud NashibiMasoud NashibiMasoud Nashibi ORCID1
1Anesthesiology Research Center, Shahid Beheshti University of Medical Sciences
*Corresponding Author: Anesthesiology Research Center, Shahid Beheshti University of Medical Sciences Email: [email protected]

Journal of Cellular & Molecular Anesthesia:Vol. 2, issue 2; e149540
Published online:May 12, 2017
Article type:Brief Communications
How to Cite:Mottaghi K, Safari F, Sezari P, Gholizadeh N, Nashibi M. Anesthetic management of patients with Klippel-Feil syndrome, a case series. J Cell Mol Anesth. 2017;2(2):e149540. doi: https://doi.org/10.22037/jcma.v2i2.15694

Abstract

Introduction: Klippel feil syndrome (KFS) is a rare entity which is characterized by failure of normal segmentation of cervical vertebrae resulting in short neck with restricted movement and cervical instability. This anomaly increases the risk of neurological damage during airway instrumentation like laryngoscopy and positioning for surgery.Case Rports: We report three patients, a 42 year old male patient with KFS who scheduled for craniocervical fusion under general anesthesia and a 6 year old girl candidate for cleft palate repair and a 26 year old woman candidate for craniocervical fusion.Conclusion: All the cases were successfully managed using fiberoptic bronchoscope in first two cases and gum elastic bougie (GEB) in the last case. All things together, Awake fiberoptic intubation could be the safest technique for airway management.

References

  • 1.
    References are in the PDF file of the article.

Copyright

© 2017, Author(s). This open-access article is available under the Creative Commons Attribution 4.0 (CC BY 4.0) International License (https://creativecommons.org/licenses/by/4.0/), which allows for unrestricted use, distribution, and reproduction in any medium, provided that the original work is properly cited.

Similar Articles

28
Nov
2015

Sitting Nasal Intubation With Fiberoptic in an Elective Mandible Surgery Under General Anesthesia

Seyyed Hassan Etemadi,
Amir Bahrami,
Ali Mohammad Farahmand,
Mohammad Mahdi Zamani

Etemadi SH, Bahrami A, Farahmand AM, Zamani MM. Sitting Nasal Intubation With Fiberoptic in an Elective Mandible Surgery Under General Anesthesia. Anesth Pain Med. 2015;5(6):e29299. doi: https://doi.org/10.5812/aapm.29299

16
Mar
2023

General Anesthesia in Schwartz-Jampel Syndrome: A Case Report

Pooya Derakhshan,
Azadeh Habibi,
Saied Amniati

Derakhshan P, Habibi A, Amniati S. General Anesthesia in Schwartz-Jampel Syndrome: A Case Report. Anesth Pain Med. 2023;13(3):e129305. doi: https://doi.org/10.5812/aapm-129305

14
Sep
2024

Anesthesia and Airway Management in a Child with Frank Ter Haar Syndrome Suspected Difficult Airway Undergoing Cardiac Surgery: A Case Report

Maryam Ghadimi,
Yasmin Chaibakhsh,
Mohsen Ziyaeifard

Ghadimi M, Chaibakhsh Y, Ziyaeifard M. Anesthesia and Airway Management in a Child with Frank Ter Haar Syndrome Suspected Difficult Airway Undergoing Cardiac Surgery: A Case Report. Anesth Pain Med. 2024;14(4):e144682. doi: https://doi.org/10.5812/aapm-144682

29
Nov
2016

Anesthesia Management of a Patient with Papillon-Lefevre Syndrome: A Case Report

Afshin Iranpour,
Ata Mahmoodpoor

Iranpour A, Mahmoodpoor A. Anesthesia Management of a Patient with Papillon-Lefevre Syndrome: A Case Report. Anesth Pain Med. 2017;7(1):e39556. doi: https://doi.org/10.5812/aapm.39556

26
Sep
2012

Cervical Decompression and Unexpected Soft Tissue Oedema: Case Report

Tiscia B. Stefanutto,
Stephen Gatt

Stefanutto T, Gatt S. Cervical Decompression and Unexpected Soft Tissue Oedema: Case Report. Anesth Pain Med. 2012;2(2):. doi: https://doi.org/10.5812/aapm.5048

Download PDF541.66 KB

Crossmark

Crossmark

Checking

Share on
Cited by
Metrics

Ordering Reprints

Articles are published under the Creative Commons license stated on each article. No permission or royalty fee is required for uses permitted by that license. CCC handles optional bulk and customized reprint orders. Any quotation covers production and delivery services only, not copyright permission. > Request Reprints from CCC 

Search Relations

Author(s):

Related Articles