Pleuropulmonary Blastoma in Children: A Case Report

authors:

avatar Azamsadat Hashemi 1 , avatar Azadeh Souzani 1 , * , avatar Amineh Souzani 1 , avatar Sara Keshavarzi 1

Hematology, Oncology and Genetic Research Center, Shahid Sadoughi University of Medical Sciences, Yazd, Iran

how to cite: Hashemi A, Souzani A , Souzani A, Keshavarzi S. Pleuropulmonary Blastoma in Children: A Case Report. Int J Cancer Manag. 2012;5(2):e80807.

Abstract

Pleuropulmonary Blastoma [PPB] is a very rare, highly aggressive and malignant tumor that originates from either the lungs or pleura. It occurs mainly in children aged less than five or six years. It has poor prognosis with three different subtypes: cystic [type I], combined cystic and solid [type II] and solid [type III]. PPB is treated with aggressive multimodal therapies including surgery and chemotherapy. We present a case of 3.5 years old boy with PPB type II successfully treated with complete surgical resection followed by neoadjuvant chemotherapy.

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