Congenital Rhabdomyosarcoma of Shoulder

authors:

avatar Ahmad Khaleghnejad Tabari 1 , * , avatar Alireza Mirshemirani 1 , avatar Mohsen Rouzrokh 1 , avatar Shahin Nariman 2 , avatar Shaghayegh Hassas-Yeganeh 1 , avatar Atoosa Gharib 3 , avatar Nasibeh Khaleghnejad-Tabari 1

Pediatric Surgery Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran
Dept. of Neonatology, Mofid Children Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran
Dept. of Pathology, Mofid Children Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran

how to cite: Khaleghnejad Tabari A , Mirshemirani A, Rouzrokh M , Nariman S , Hassas-Yeganeh S, et al. Congenital Rhabdomyosarcoma of Shoulder. Int J Cancer Manag. 2012;5(3):e80822. 

Abstract

A 16-day-old female was referred with congenital swelling on her right shoulder. On examination, there was a hard, round, ecchymotic, nontender, slightly movable, warm and shiny 10x15 cm mass on the right axillary pits which was extended to the right side of neck and chest wall. The mass separated the shoulder from the chest wall causing paralysis of right hand. Chest X-ray, ultrasound and MRI with contrast demonstrated a soft tissue mass suspected to be a hemangioma. The mass rapidly increased in size despite aggressive steroid therapy with rupture and bleeding. On the 45th post natal day the baby was taken to operating room to control the bleeding and if possible total excision of the mass. The mass was separated easily from the surrounding tissue and was excised along with right upper extremity. At the end of surgery the baby had cardiac arrest, and apparently died of Disseminated Intravascular Coagulation (DIC). The final pathology report was Rhabdomyosarcoma (RMS).

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