Periodic Fever: A Review on Clinical, Management and Guideline for Iranian Patients - Part II

Zahra  Ahmadinejad; Sedigeh  Mansouri; Vahid Ziaee; Yahya  Aghighi; Mohammad-Hassan  Moradinejad; Fatemeh- Fereshteh Mehregan

IJ Pediatrics

The Scientific Journal of Growth & Development Research Center

Outlines

Abstract
References
Copyright

Periodic Fever: A Review on Clinical, Management and Guideline for Iranian Patients - Part II

Author(s):

Zahra Ahmadinejad¹,

Sedigeh Mansouri²,

Vahid Ziaee^3,*,

Yahya Aghighi⁴,

Mohammad-Hassan Moradinejad⁵,

Fatemeh- Fereshteh Mehregan⁶

IJ Pediatrics:Vol. 24, issue 3; 229-240

Published online:May 05, 2014

Article type:Review Article

Received:Sep 20, 2013

Accepted:Jan 03, 2014

How to Cite:Zahra AhmadinejadSedigeh MansouriVahid ZiaeeYahya AghighiMohammad-Hassan MoradinejadFatemeh- Fereshteh Mehreganet al.Periodic Fever: A Review on Clinical, Management and Guideline for Iranian Patients - Part II.Iran J Pediatr.24(3):229-240.

Abstract

Periodic fever syndromes are a group of diseases characterized by episodes of fever with healthy intervals between febrile episodes. In the first part of this paper, we presented a guideline for approaching patients with periodic fever and reviewed two common disorders with periodic fever in Iranian patients including familial Mediterranean fever (FMF) and periodic fever syndromes except for periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA). In this part, we review other autoinflammatory disorders including hyper IgD, tumor necrosis factor receptor–associated periodic syndrome (TRAPS), cryopyrin associated periodic syndromes, autoinflammatory bone disorders and some other rare autoinflammatory disorders such as Sweet’s and Blau syndromes. In cryopyrin associated periodic syndromes group, we discussed chronic infantile neurologic cutaneous and articular (CINCA) syndrome, Muckle-Wells syndrome and familial cold autoinflammatory syndrome. Autoinflammatory bone disorders are categorized to monogenic disorders such as pyogenic arthritis, pyoderma ;gangraenosum and acne (PAPA) syndrome, the deficiency of interleukine-1 receptor antagonist (DIRA) and Majeed syndrome and polygenic background or sporadic group such as chronic recurrent multifocal osteomyelitis (CRMO) or synovitis, acne, pustulosis, hyperostosis and osteitis (SAPHO) syndrome are classified in sporadic group. Other autoinflammatory syndromes are rare causes of periodic fever in Iranian system registry.

Keywords

Periodic Fever

Hyper IgD

TRAPS

Autoinflammatory Bone Disorder

Cryopyrin Associated Periodic Syndromes

Sweet’s Syndrome

Blau Syndrome

Fulltext

Click here to download PDF.

References

1.
References are available on the PDF.

comments