Idiopathic Right Atrial Enlargement (Volume: 700 cc) in a Young Man: A Case Report

authors:

avatar Zahra Khajali ORCID 1 , avatar Fateme Jorfi ORCID 1 , * , avatar Mozhghan Parsaee ORCID 1 , avatar Mohammad Kasaei 1 , avatar Mehrdad Jafarifesharaki ORCID 2

Rajaei Heart Medical and Research Center, Iran University of Medical Sciences, Tehran, IR Iran
School of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, IR Iran
International Cardiovascular Research Journal: Vol.13, issue 4; e92367
published online: December 01, 2019
article type: Case Report
received: April 16, 2019
accepted: October 05, 2019

how to cite: Khajali Z, Jorfi F, Parsaee M, Kasaei M, Jafarifesharaki M. Idiopathic Right Atrial Enlargement (Volume: 700 cc) in a Young Man: A Case Report. Int Cardiovasc Res J. 2019;13(4):e92367. 

Abstract

Idiopathic right atrial dilation is known as a congenital anomaly in the absence of obvious causes that produce right ventricular pressure or volume overload. Congenital giant right atrium can cause functional tricuspid regurgitation, arrhythmia, and right-sided heart failure. A massive Idiopathic Dilation of Right Atrium (IDRA) was reported in a 30-year-old man presented with intermittent palpitation and dyspnea on effort. Transthoracic echocardiography revealed huge right atrium leading to severe tricuspid regurgitation, moderate right ventricular enlargement with moderate dysfunction, and no evidence of other valvular heart diseases increasing the right ventricular pressure or volume, left to right shunt, and Ebstein anomaly. Cardiac Magnetic Resonance Imaging (MRI) confirmed the right atrial enlargement. The estimated right atrium volume by MRI was about 700 mL. With regard to the patient’s symptoms, he was scheduled for surgical treatment. The patient underwent partial surgical resection of the dilated right atrium wall and mechanical tricuspid valve replacement because the tricuspid valve was unrepairable on the operation table. Idiopathic right atrial enlargement is a very rare disease and may be easily confused with other anomalies that lead to right atrial enlargement, such as Ebstein anomaly. Hence, the probability of this pathology should be kept in mind when the usual etiologies of right atrial enlargement are excluded. Partial surgical resection of the dilated right atrium is an effective therapeutic option in symptomatic patients.

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Video 1. The Huge Inappropriate Right Atrial Enlargement Seen in Apical Four-Chamber Echocardiographic View

https://neoscriber.org/cdn/serve/314b8/29be36d42f8a9f93df24558328492ea6469bbfc6/vid%201.avi

 

Video 2. Axial Cine MR Showing Severe Right Atrial Enlargement and Severe Tricuspid Regurgitation with Partial Distortion due to Severe Right Atrial Dilation without Apical Displacement of Any of Its Leaflets

https://neoscriber.org/cdn/serve/314b8/29be36d42f8a9f93df24558328492ea6469bbfc6/vid%202.avi

References

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    The references are available in PDF.