Crouzon Syndrome: a fibroblast growth factor receptor 2 gene mutation

Author(s):
Farhad SafariFarhad SafariFarhad Safari ORCID1,*, Kamran MottaghiKamran MottaghiKamran Mottaghi ORCID1, Rofeideh FallahinejadghajariRofeideh Fallahinejadghajari1, Masoud NashibiMasoud NashibiMasoud Nashibi ORCID1
1Anesthesiology Research Center, Shahid Beheshti University of Medical Sciences
*Corresponding Author: Anesthesiology Research Center, Shahid Beheshti University of Medical Sciences Email: [email protected]

Journal of Cellular & Molecular Anesthesia:Vol. 2, issue 1; e149531
Published online:Jan 01, 2017
Article type:Brief Communications
How to Cite:Safari F, Mottaghi K, Fallahinejadghajari R, Nashibi M. Crouzon Syndrome: a fibroblast growth factor receptor 2 gene mutation. J Cell Mol Anesth. 2017;2(1):e149531. doi: https://doi.org/10.22037/jcma.v2i1.14905

Abstract

Crouzon syndrome is a rare autosomal dominant premature cranyosynostosis, caused by fibroblast growth factor receptor 2 gene mutation on chromosome 10. The predominant skull and facial malformations with potential compromise airway make the crouzon syndrome a demanding issue for anesthesiologists and surgeons, required dynamic team work. In this report we describe a child, a known case of Crouzon syndrome who was a candidate for optic nerve decompression through endoscopic surgery. The anesthetic considerations and management are presented.Key words: Crouzon Syndrome, FGFR2 gene, Difficult Intubation, Anesthesia

References

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    References are in the PDF file of the article.

Copyright

© 2017, Author(s). This open-access article is available under the Creative Commons Attribution 4.0 (CC BY 4.0) International License (https://creativecommons.org/licenses/by/4.0/), which allows for unrestricted use, distribution, and reproduction in any medium, provided that the original work is properly cited.

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